Frataxin Antibody / FXN [Mouse Monoclonal] from NSJ Bioreagents

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Supplier Page from
NSJ Bioreagents for
Frataxin Antibody / FXN [Mouse Monoclonal]

Description

Frataxin is a nuclear-encoded mitochondrial protein implicated in Friedreich's ataxia (FRDA), a human autosomal recessive neurodegenerative disease. Lack of Frataxin causes iron to accumulate in the mitochondrial matrix suggesting that Frataxin is involved in mitochondrial iron homeostasis and possibly in iron transport. Frataxin has an alpha-beta fold consisting of two helices flanking an antiparallel beta sheet